GPCRDB: Swiss-Prot entry
ID PRIO_CRIMI STANDARD; PRT; 254 AA.
AC Q60468;
DT 15-JUL-1998 (Rel. 36, Created)
DT 15-JUL-1998 (Rel. 36, Last sequence update)
DT 05-JUL-2004 (Rel. 44, Last annotation update)
DE Major prion protein precursor (PrP) (PrP27-30) (PrP33-35C).
GN Name=PRNP;
OS Cricetulus migratorius (Armenian hamster).
OC Eukaryota; Metazoa; Chordata; Craniata; Vertebrata; Euteleostomi;
OC Mammalia; Eutheria; Rodentia; Sciurognathi; Muridae; Cricetinae;
OC Cricetulus.
OX NCBI_TaxID=10032;
RN [1]
RP NUCLEOTIDE SEQUENCE.
RC TISSUE=Brain;
RX MEDLINE=90158578; PubMed=2406562 [NCBI, ExPASy, EBI, Israel, Japan];
RA Lowenstein D.H., Butler D.A., Westaway D., McKinley M.P.,
RA DeArmond S.J., Prusiner S.B.;
RT "Three hamster species with different scrapie incubation times and
RT neuropathological features encode distinct prion proteins.";
RL Mol. Cell. Biol. 10:1153-1163(1990).
CC -!- FUNCTION: The function of PrP is not known. PrP is encoded in the
CC host genome and is expressed both in normal and infected cells.
CC -!- SUBUNIT: PrP has a tendency to aggregate yielding polymers called
CC "rods".
CC -!- SUBCELLULAR LOCATION: Attached to the membrane by a GPI-anchor.
CC -!- DISEASE: PrP is found in high quantity in the brain of humans and
CC animals infected with the degenerative neurological diseases kuru,
CC Creutzfeldt-Jakob disease (CJD), Gerstmann-Straussler syndrome
CC (GSS), scrapie, bovine spongiform encephalopathy (BSE),
CC transmissible mink encephalopathy (TME), etc.
CC -!- SIMILARITY: Belongs to the prion family.
CC --------------------------------------------------------------------------
CC This Swiss-Prot entry is copyright. It is produced through a collaboration
CC between the Swiss Institute of Bioinformatics and the EMBL outstation -
CC the European Bioinformatics Institute. There are no restrictions on its
CC use as long as its content is in no way modified and this statement is not
CC removed.
CC --------------------------------------------------------------------------
DR EMBL; M33959; AAA37014.1; -. [EMBL / GenBank / DDBJ] [CoDingSequence]
DR HSSP; P04925; 1AG2. [HSSP ENTRY / SWISS-3DIMAGE / PDB]
DR InterPro; IPR000817; Prion.
DR InterPro; Graphical view of domain structure.
DR Pfam; PF00377; Prion; 1.
DR Pfam; PF03991; Prion_octapep; 6.
DR Pfam; Graphical view of domain structure.
DR PRINTS; PR00341; PRION.
DR PROSITE; PS00291; PRION_1; 1.
DR PROSITE; PS00706; PRION_2; 1.
DR ProDom [Domain structure / List of seq. sharing at least 1 domain]
DR HOVERGEN [Family / Alignment / Tree]
DR BLOCKS; Q60468.
DR ProtoNet; Q60468.
DR ProtoMap; Q60468.
DR PRESAGE; Q60468.
DR DIP; Q60468.
DR ModBase; Q60468.
DR SMR; Q60468.
DR SWISS-2DPAGE; GET REGION ON 2D PAGE.
KW Glycoprotein; GPI-anchor; Lipoprotein; Prion; Repeat; Signal.
FT SIGNAL 1 22 By similarity.
FT CHAIN 23 231 Major prion protein.
FT PROPEP 232 254 Removed in mature form.
FT LIPID 231 231 GPI-anchor amidated serine.
FT DOMAIN 90 231 PrP27-30 (protease resistant core).
FT CARBOHYD 181 181 N-linked (GlcNAc...) (By similarity).
FT CARBOHYD 197 197 N-linked (GlcNAc...) (By similarity).
FT DISULFID 179 214 By similarity.
FT DOMAIN 51 91 5 X 8 AA tandem repeats of P-H-G-G-G-W-G-
FT Q.
FT REPEAT 51 59 1.
FT REPEAT 60 67 2.
FT REPEAT 68 75 3.
FT REPEAT 76 83 4.
FT REPEAT 84 91 5.
SQ SEQUENCE 254 AA; 27855 MW; 7B963FC6F77F9D0F CRC64;
MANLSYWLLA LFVATWTDVG LCKKRPKPGG WNTGGSRYPG QGSPGGNRYP PQGGGTWGQP
HGGGWGQPHG GGWGQPHGGG WGQPHGGGWG QGGGTHNQWN KPNKPKTSMK HMAGAAAAGA
VVGGLGGYML GSAMSRPMLH FGNDWEDRYY RENMNRYPNQ VYYRPVDQYN NQNNFVHDCV
NITIKQHTVT TTTKGENFTE TDVKMMERVV EQMCVTQYQK ESQAYYDGRR SSAVLFSSPP
VILLISFLIF LIVG
//