GPCRDB: Swiss-Prot entry
ID PRIO_CAMDR STANDARD; PRT; 255 AA.
AC P79141;
DT 01-NOV-1997 (Rel. 35, Created)
DT 01-NOV-1997 (Rel. 35, Last sequence update)
DT 05-JUL-2004 (Rel. 44, Last annotation update)
DE Major prion protein precursor (PrP).
GN Name=PRNP; Synonyms=PRP;
OS Camelus dromedarius (Dromedary) (Arabian camel).
OC Eukaryota; Metazoa; Chordata; Craniata; Vertebrata; Euteleostomi;
OC Mammalia; Eutheria; Cetartiodactyla; Tylopoda; Camelidae; Camelus.
OX NCBI_TaxID=9838;
RN [1]
RP NUCLEOTIDE SEQUENCE.
RX MEDLINE=98019099; PubMed=9358067 [NCBI, ExPASy, EBI, Israel, Japan]; DOI=10.1016/S0378-1119(97)00382-X;
RA Kaluz S., Kaluzova M., Flint A.P.F.;
RT "Sequencing analysis of prion genes from red deer and camel.";
RL Gene 199:283-286(1997).
CC -!- FUNCTION: The function of PrP is not known. PrP is encoded in the
CC host genome and is expressed both in normal and infected cells.
CC -!- SUBUNIT: PrP has a tendency to aggregate yielding polymers called
CC "rods".
CC -!- SUBCELLULAR LOCATION: Attached to the membrane by a GPI-anchor.
CC -!- DISEASE: PrP is found in high quantity in the brain of humans and
CC animals infected with the degenerative neurological diseases kuru,
CC Creutzfeldt-Jakob disease (CJD), Gerstmann-Straussler syndrome
CC (GSS), scrapie, bovine spongiform encephalopathy (BSE),
CC transmissible mink encephalopathy (TME), etc.
CC -!- SIMILARITY: Belongs to the prion family.
CC --------------------------------------------------------------------------
CC This Swiss-Prot entry is copyright. It is produced through a collaboration
CC between the Swiss Institute of Bioinformatics and the EMBL outstation -
CC the European Bioinformatics Institute. There are no restrictions on its
CC use as long as its content is in no way modified and this statement is not
CC removed.
CC --------------------------------------------------------------------------
DR EMBL; Y09760; CAA70901.1; -. [EMBL / GenBank / DDBJ] [CoDingSequence]
DR HSSP; P23907; 1G04. [HSSP ENTRY / SWISS-3DIMAGE / PDB]
DR InterPro; IPR000817; Prion.
DR InterPro; Graphical view of domain structure.
DR Pfam; PF00377; Prion; 1.
DR Pfam; PF03991; Prion_octapep; 5.
DR Pfam; Graphical view of domain structure.
DR PRINTS; PR00341; PRION.
DR PROSITE; PS00291; PRION_1; 1.
DR PROSITE; PS00706; PRION_2; 1.
DR ProDom [Domain structure / List of seq. sharing at least 1 domain]
DR HOVERGEN [Family / Alignment / Tree]
DR BLOCKS; P79141.
DR ProtoNet; P79141.
DR ProtoMap; P79141.
DR PRESAGE; P79141.
DR DIP; P79141.
DR ModBase; P79141.
DR SMR; P79141.
DR SWISS-2DPAGE; GET REGION ON 2D PAGE.
KW Glycoprotein; GPI-anchor; Lipoprotein; Membrane; Prion; Repeat;
KW Signal.
FT SIGNAL 1 24 By similarity.
FT CHAIN 25 233 Major prion protein.
FT PROPEP 234 255 Removed in mature form (Potential).
FT DOMAIN 54 94 5 X 8 AA tandem repeats of P-H-G-G-G-W-G-
FT Q.
FT REPEAT 54 62 1.
FT REPEAT 63 70 2.
FT REPEAT 71 78 3.
FT REPEAT 79 86 4.
FT REPEAT 87 94 5.
FT DISULFID 182 217 By similarity.
FT LIPID 233 233 GPI-anchor amidated alanine (Potential).
FT CARBOHYD 184 184 N-linked (GlcNAc...) (Potential).
FT CARBOHYD 200 200 N-linked (GlcNAc...) (Potential).
SQ SEQUENCE 255 AA; 27595 MW; FABB2DBFA333E494 CRC64;
MVKSHMGSWI LVLFVVTWSD VGLCKKRPKP GGGWNTGGSR YPGQGSPGGN RYPPQGGGGW
GQPHGGGWGQ PHGGGWGQPH GGGWGQPHGG GWGQGGGAHG QWNKPSKPKT SMKHVAGAAA
AGAVVGGLGG YMLGSAMSRP LIHFGNDYED RYYRENMYRY PNQVYYKPVD QYSNQNSFVH
DCVNITVKQH TVTTTTKGEN FTETDVKMME RVVEQMCITQ YQREYQASYG RGASVIFSSP
PVILLISFLI FLIVG
//