GPCRDB: Swiss-Prot entry
ID PRIO_CALMO STANDARD; PRT; 241 AA.
AC P40248;
DT 01-FEB-1995 (Rel. 31, Created)
DT 01-FEB-1995 (Rel. 31, Last sequence update)
DT 05-JUL-2004 (Rel. 44, Last annotation update)
DE Major prion protein precursor (PrP) (PrP27-30) (PrP33-35C) (Fragment).
GN Name=PRNP;
OS Callicebus moloch (Dusky titi).
OC Eukaryota; Metazoa; Chordata; Craniata; Vertebrata; Euteleostomi;
OC Mammalia; Eutheria; Primates; Platyrrhini; Cebidae; Callicebinae;
OC Callicebus.
OX NCBI_TaxID=9523;
RN [1]
RP NUCLEOTIDE SEQUENCE.
RX MEDLINE=95139066; PubMed=7837269 [NCBI, ExPASy, EBI, Israel, Japan];
RA Schatzl H.M., Dacosta M., Taylor L., Cohen F.E., Prusiner S.B.;
RT "Prion protein gene variation among primates.";
RL J. Mol. Biol. 245:362-374(1995).
CC -!- FUNCTION: The function of PrP is not known. PrP is encoded in the
CC host genome and is expressed both in normal and infected cells.
CC -!- SUBUNIT: PrP has a tendency to aggregate yielding polymers called
CC "rods".
CC -!- SUBCELLULAR LOCATION: Attached to the membrane by a GPI-anchor.
CC -!- DISEASE: PrP is found in high quantity in the brain of humans and
CC animals infected with the degenerative neurological diseases kuru,
CC Creutzfeldt-Jakob disease (CJD), Gerstmann-Straussler syndrome
CC (GSS), scrapie, bovine spongiform encephalopathy (BSE),
CC transmissible mink encephalopathy (TME), etc.
CC -!- SIMILARITY: Belongs to the prion family.
CC --------------------------------------------------------------------------
CC This Swiss-Prot entry is copyright. It is produced through a collaboration
CC between the Swiss Institute of Bioinformatics and the EMBL outstation -
CC the European Bioinformatics Institute. There are no restrictions on its
CC use as long as its content is in no way modified and this statement is not
CC removed.
CC --------------------------------------------------------------------------
DR EMBL; U08312; AAC50100.1; -. [EMBL / GenBank / DDBJ] [CoDingSequence]
DR PIR; S71048; S71048.
DR HSSP; P23907; 1G04. [HSSP ENTRY / SWISS-3DIMAGE / PDB]
DR InterPro; IPR000817; Prion.
DR InterPro; Graphical view of domain structure.
DR Pfam; PF00377; Prion; 1.
DR Pfam; PF03991; Prion_octapep; 6.
DR Pfam; Graphical view of domain structure.
DR PRINTS; PR00341; PRION.
DR PROSITE; PS00291; PRION_1; 1.
DR PROSITE; PS00706; PRION_2; 1.
DR HOVERGEN [Family / Alignment / Tree]
DR BLOCKS; P40248.
DR ProtoNet; P40248.
DR ProtoMap; P40248.
DR PRESAGE; P40248.
DR DIP; P40248.
DR ModBase; P40248.
DR SMR; P40248.
DR SWISS-2DPAGE; GET REGION ON 2D PAGE.
KW Glycoprotein; GPI-anchor; Lipoprotein; Membrane; Prion; Repeat;
KW Signal.
FT NON_TER 1 1
FT SIGNAL <1 15 By similarity.
FT CHAIN 16 223 Major prion protein.
FT PROPEP 224 >241 Removed in mature form (By similarity).
FT DISULFID 172 207 By similarity.
FT LIPID 223 223 GPI-anchor amidated serine (By
FT similarity).
FT CARBOHYD 174 174 N-linked (GlcNAc...) (Potential).
FT CARBOHYD 190 190 N-linked (GlcNAc...) (Potential).
FT DOMAIN 44 84 5 X 8 AA tandem repeats of P-H-G-G-G-W-G-
FT Q.
FT REPEAT 44 52 1.
FT REPEAT 53 60 2.
FT REPEAT 61 68 3.
FT REPEAT 69 76 4.
FT REPEAT 77 84 5.
FT NON_TER 241 241
SQ SEQUENCE 241 AA; 26373 MW; C6D2013EE7CAEC93 CRC64;
MLVLFVATWS DLGLCKKRPK PGGWNTGGSR YPGQGSPGGN RYPPQGGGSW GQPHGGGWGQ
PHGGGWGQPH GGGWGQPHGG GWGQGGGTHN QWNKPSKPKT NMKHVAGAAA AGAVVGGLGG
YMLGSAMSRP LIHFGNDYED RYYRENMYRY PNQVYYRPVD QYSNQNNFVH DCVNITIKQH
TVTTTTKGEN FTETDVKMME RVVEQMCITQ YEKESQAYYQ RGSSMVLFSS PPVILLISFL
I
//